Chiyero chekuongorora kuchangobva kuberekwa, chinowanzonzi chiratidzo chePKU, chiratidzo cheropa chinotarisa zvinetso zvakasiyana-siyana mumwana achangoberekwa. Chirongwa chePKU chinoitwa nekudzivirira chidendwe checheche uye kubvumira madonhwe akawanda eropa achidonhera pane kadhi rakakosha. Chiyero chinopesana nehurumende, nedzimwe nyika dziri kutsvaga zvinetso zvakawanda kupfuura vamwe.
Kuongorora kwePKU kunofanira kuitwa mushure mokunge mucheche ari maawa makumi maviri nemaviri kusvika makumi maviri nemashanu asi mazuva manomwe ekutanga ehupenyu.
Inowanzoitwa musati mwana achangoberekwa achibva kuchipatara. Vacheche vakaberekerwa pamba kana mune imwe nzvimbo yekunze kwechipatara vanofanira kuonana nevanamukoti vavo kana vanachiremba vevana kuti vawane mabhii ekupedzisira anokwanisa kuedza.
Sei Chirwere Chisina Kuzvarwa Chichinziwo PKU Test?
Muna 1963, Dr. Robert Guthrie akatanga chirongwa chakanaka uye chisina mari chePKU, kana phenylketonuria, mucheche. Nokufamba kwenguva, muedzo wakafanana wakashandiswa kutarisa zvimwe zvinetso zvakawanda. Kunyange zvazvo muedzo wekuongororwa uchangobva kuberekwa iye zvino unotarisa zvinetso zvakasiyana-siyana makumi mashanu mune dzimwe nyika, inenge ichiwanzonzi Test PKU.
Chii Chinogona Kuongororwa PKU?
Kunyange zvazvo kuongorora kwePKU kwakasiyana nedzimwe nyika, nyika dzose dzinoshandisa kuongorora kuzvarwa patsva kuongororwa zvinetso 21 zvakasiyana-siyana, kusanganisira:
- PKU
- Congenital hypothyroidism
- Galactosemia
Nzvimbo dzakawanda dzinoshandisa chiratidzo chePKU kuti chiongorore zvinetso zvekare nezvimwe kuongororwa zvirwere zvinopfuura 50 zvakasiyana.
Zvakawanda zvezvinetso izvi zvinoshandisa muviri, zvinoreva kuti zvinokanganisa nzira iyo masero anoita simba.
Nei Chiitiko chePKU Chinokosha?
Chirongwa chePKU chinotarisa zvinetso zvinogona kukonzera matambudziko makuru ezvehutano kana zvisati zvarapwa. Zvimwe zvevhiringidzi zvinogona kuva zvakakomba zvikuru kana kunyange kutyisa upenyu muvhiki yekutanga yehupenyu kana zvisingawanikwi uye zvakarapwa pakarepo.
Vamwe havaratidzi zviratidzo kwemwedzi kana kwemakore, uye zviratidzo zvingaita sezvimwe zvinetso.
Iko Test PKU yakasiyana sei muNICU?
Zvose kusasarudzwa kwevavengi uye zvinetso zvehutano hweNICU zvinogona kuita kuti zviitiko zvekuzvarwa patsva kuongorora zvive zvakaoma kududzira. NICU varwere vangave vachida kuongororwa kanopfuura kamwe kuitira kuti zvive nyore kunzwisisa.
Vana vachembera uye vana vacheche vanodikanwa neNICU kuchengetwa vane nyaya dzakawanda dzinogona kukanganisa kuongorora kuzvarwa patsva:
- Kudya kwemazuva mashoma: Vana vakawanda veNICU havawaniki mazai emukaka pakarepo, pamusana pengozi yeNET, chido, kana zvimwe zvinhu. Kunze kwekunge nzira dzekuongorora dzakafambiswa dzichishandiswa, zviitiko zvekuongorora kwePKU zvakanyatsonaka mushure mokunge mwana ari kugamuchira mukaka wekudya kwemaawa masere kusvika ma48 asi mukati memazuva manomwe ehupenyu.
- Mishonga inorwisa mabhakitiriya: Mishonga inorwisa mabhakitiriya inogona kukanganisa kunyatsoratidzwa kweimwe mimwe miedzo inoshandiswa pamuedzo wePKU.
- Kwose parenteral nutrition (TPN) : TPN inogona kukanganisa kusarurama kwevamwe vana vanenge vachangoberekwa kuongorora.
- Kuwedzerwa ropa: Nokuti kuwedzerwa kweropa kunotsiva rimwe ropa remwana pachake neropa rekuenzaniswa kwakasiyana, kuwedzerwa ropa kunogona kukanganisa kuita kuti PKU iongorore zvishoma.
- Nhamba dzakakwirira dze hypothyroidism: Vana vacheche vasati vasvika vane mazinga akawandisa e hypothyroidism kupfuura nguva yevana. Izvi zvinowanzotora nguva pfupi uye zvinowedzera zviri nani pakarepo pasina zvigaro zvisingagumi, asi zvinogona kukanganisa kukura uye kubudirira kana zvisingaongororwe zvakanyanya.
Kana mwana wako asati apera kana kupedza nguva muNICU, zvichida akawana zvimwe zvepamusoro apa kana kuti ane nguva ye hypothyroidism. Vashandi veNICU vanowanzoita imwe chirongwa chePKU mushure mekugadzirira kupindira, uye kuongorora zvakare kunoda kutorwa pane imwe nguva gare gare. Kudzokorora kuongorora kuchabatsirawo kuziva kana hypothyroidism inoda kurapwa.
Vana vasati vasvika vanowanzogamuchira mhinduro dzavo zvakare muNICU. Kana waive neine mwana mwana waive muNICU kwenguva pfupi, bvunza chiremba wevana kana chirwere chePKU chichifanira kudzokororwa, uye kana.
Zvakadini kana muNewborn Screening Test / PKU Test yakakosha?
Kana muchecheche wako wechecheche wakanga wakanaka kune PKU kana chimwe chirwere, kuongororwa kunoitwa kuchaitwa kuti uite kuti unenge uchifungidzirwa kuongororwa. Mimwe mitsva yekuongorora inenge ichangobva kuongorora inhema-zvipo, naizvozvo mwana wako angasave neine mhosva yekufungidzirwa chirwere. Kana chirwere chichionekwa, kurapa kuchazokurukurwa uye kutanga.
Sources:
Bryant, Kristin RN BSN MSN; Horns, Kimberly RNC, NNP, PHD; Longo, Nicola MD, PhD; Schiefelbein, Julieanne MappSc, RNC, MA, RM, PNP, NNP. "Primer pamusoro peNewborn Screening." Kufambira Mberi Mukurera Neonatal October 2004; 4, 306-317.
March weDhimes. "Kuzvarwa Kuchangobva Kuongorora Kuedzwa."
March weDhimes. "States Wedzera Nhepfenyuro Kuongorora Kuupenyu-Kutyisidzira Kutyisa."